{"id":27113,"date":"2025-07-18T09:02:42","date_gmt":"2025-07-18T09:02:42","guid":{"rendered":"https:\/\/neuronup.com\/?p=27113"},"modified":"2025-07-18T09:02:42","modified_gmt":"2025-07-18T09:02:42","slug":"syndrome-de-tourette","status":"publish","type":"post","link":"https:\/\/neuronup.com\/fr\/maladies-rares\/syndrome-de-tourette\/","title":{"rendered":"D\u00e9construire le syndrome de Tourette"},"content":{"rendered":"\n<p class=\"has-xl-font-size\">Avez-vous entendu parler du <strong>syndrome de Tourette<\/strong>? En Espagne, il est encore consid\u00e9r\u00e9 comme une maladie rare en raison de sa pr\u00e9valence dans la population, cependant des \u00e9tudes internationales indiquent qu\u2019il s\u2019agit en r\u00e9alit\u00e9 d\u2019une condition beaucoup plus fr\u00e9quente qu\u2019on ne le pensait. Cet article est d\u00e9di\u00e9 \u00e0 d\u00e9mystifier cette et d\u2019autres id\u00e9es re\u00e7ues qui circulent encore \u00e0 son sujet. D\u00e9construisons donc le<strong> syndrome de Tourette<\/strong>.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">Qu&rsquo;est-ce que le syndrome de Tourette ?<\/h2>\n\n\n\n<p>Selon les crit\u00e8res diagnostiques internationaux, le syndrome de Tourette est un<strong> trouble primaire du mouvement dont la caract\u00e9ristique principale est la pr\u00e9sence chronique de tics<\/strong> [3,4], bien qu\u2019il soit souvent associ\u00e9 \u00e0 d\u2019autres troubles tels que le TOC ou le TDAH [1].<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">Qu\u2019est-ce qui d\u00e9finit un tic ?<\/h3>\n\n\n\n<p>Comme il a \u00e9t\u00e9 soulign\u00e9, le mot <strong><em>tic<\/em><\/strong> d\u00e9rive de l\u2019italien <em>ticchio<\/em> [5] qui signifie <em>caprice<\/em> au sens de d\u00e9sir, luxe, extravagance [6, 7]. Bien loin d\u2019\u00eatre un caprice ou un d\u00e9sir de la personne qui les manifeste, les tics sont <strong><em>mouvements ou vocalisations<\/em> qu\u2019on <em>r\u00e9alise de fa\u00e7on involontaire<\/em><\/strong>. Bien qu\u2019ils puissent para\u00eetre extravagants en raison de leur <em>intensit\u00e9, fr\u00e9quence ou r\u00e9p\u00e9tition exag\u00e9r\u00e9es, et de leur d\u00e9contextualisation<\/em> ou sans lien avec les situations, ce sont des comportements qui <em>ne sont pas dirig\u00e9s vers un objectif<\/em>, contrairement aux mouvements volontaires [8] ou \u00e0 l\u2019\u00e9mission volontaire de mots ou de sons.<\/p>\n\n\n\n<div style=\"height:50px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"wp-block-group br-0111 has-primary-background-color has-background has-dark-background has-sm-padding-top has-sm-padding-left has-sm-padding-right has-xxl-margin-top\"><div class=\"wp-block-group__inner-container is-layout-constrained wp-block-group-is-layout-constrained\">\n<div class=\"wp-block-columns is-layout-flex wp-container-core-columns-is-layout-9d6595d7 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\">\n<figure class=\"wp-block-image size-full desktop-position-absolute desktop-bottom-0 mobile-width-50 mobile-m-inline-auto has-xl-margin-top\"><img decoding=\"async\" width=\"292\" height=\"338\" src=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/10\/certificat-produit.webp\" alt=\"\" class=\"wp-image-31568\" srcset=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/10\/certificat-produit-259x300.webp 259w, https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/10\/certificat-produit.webp 292w\" sizes=\"(max-width: 292px) 100vw, 292px\" \/><\/figure>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\">\n<h2 class=\"wp-block-heading has-white-color has-text-color\"><strong>Abonnez-vous<\/strong> <br>\u00e0 notre <br>Newsletter<\/h2>\n\n\n\n<div class=\"wp-block-buttons is-layout-flex wp-block-buttons-is-layout-flex\">\n<div class=\"wp-block-button--1\" style=\"--button-outline-color:var(--color-white);--button-outline-color-hover:rgba(0,0,0,0.8);\"><a class=\"wp-block-button__link button button-outline   wp-element-button\" href=\"https:\/\/neuronup.com\/fr\/newsletter\/\">Abonnez-vous<\/a><\/div>\n\n<\/div>\n\n\n\n<div style=\"height:40px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n<\/div>\n<\/div>\n<\/div><\/div>\n\n\n\n\n<div style=\"height:50px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h2 class=\"wp-block-heading\">D\u00e9construire le Tourette<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Plus qu&rsquo;un syndrome, c&rsquo;est un trouble du spectre<\/strong>. Divers syndromes ou sous-types de Tourette ont \u00e9t\u00e9 d\u00e9crits [1,9], raison pour laquelle il est d\u00e9sormais jug\u00e9 plus appropri\u00e9 de parler de <em>trouble du spectre de Tourette<\/em> que de syndrome de Tourette [10].<\/li>\n\n\n\n<li><strong>Dire des obsc\u00e9nit\u00e9s n&rsquo;est pas fr\u00e9quent dans le Tourette<\/strong>. La <em>coprolalie<\/em> (dire des mots obsc\u00e8nes involontairement et sans intention d&rsquo;offenser [1,10]) est l&rsquo;un des sympt\u00f4mes les plus m\u00e9diatis\u00e9s du Tourette, en partie \u00e0 cause de sa diffusion au cin\u00e9ma et dans les m\u00e9dias. Bien qu&rsquo;elle puisse \u00eatre l&rsquo;une de ses manifestations les plus spectaculaires, c&rsquo;est une caract\u00e9ristique pr\u00e9sente chez <em>moins d&rsquo;un cinqui\u00e8me des personnes concern\u00e9es<\/em> [11].<\/li>\n\n\n\n<li><strong>Une cr\u00e9ativit\u00e9 musicale particuli\u00e8re<\/strong>. Bien qu\u2019il ne semble pas exister de relation lin\u00e9aire entre l\u2019exc\u00e8s de dopamine sous-jacent au Tourette et la cr\u00e9ativit\u00e9, les \u00e9tudes mettent en \u00e9vidence une association entre le trouble de Tourette et la cr\u00e9ativit\u00e9 musicale [12].<\/li>\n\n\n\n<li><strong>Son origine n&rsquo;est pas psychologique.<\/strong> Bien qu&rsquo;on ait initialement consid\u00e9r\u00e9 que la cause du Tourette \u00e9tait psychologique, cette th\u00e9orie est devenue obsol\u00e8te [1], car les preuves indiquent une \u00e9tiologie incluant des influences \u00e0 la fois <strong>g\u00e9n\u00e9tiques<\/strong> et <strong>environnementales<\/strong> [1].<\/li>\n<\/ul>\n\n\n\n<h3 class=\"wp-block-heading has-xl-font-size\" style=\"font-style:normal;font-weight:400\">Bibliographie<\/h3>\n\n\n\n<ol class=\"wp-block-list\">\n<li class=\"has-xs-font-size\"><em>Robertson, M. M. (2012). The Gilles De LaTourette syndrome: the current status. Archives Of Disease In Childhood \u2013 Education And Practice, 97(5), 166-175. http:\/\/dx.doi.org\/10.1136\/archdischild-2011-300585<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Robertson, M. M., Eapen, V., &amp; Cavanna, A. E. (2009). The international prevalence, epidemiology, and clinical phenomenology of Tourette syndrome: A cross-cultural perspective. Journal Of Psychosomatic Research, 67(6), 475-483. http:\/\/dx.doi.org\/10.1016\/j.jpsychores.2009.07.010<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>American Psychiatric Association (2013). Diagnostic and Statistical Manual of Mental Disorders: DSM-5 (5th ed.) Washington D.C.: Autor.<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Organisation mondiale de la Sant\u00e9 (1992) Classification internationale des maladies et probl\u00e8mes de sant\u00e9 connexes: CIM-10 (10e r\u00e9vision). Gen\u00e8ve: Auteur<\/em>.<\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Varsemanas, D. R. (septembre 2002). L\u2019incidence du stress et les objectifs de la th\u00e9rapie psychologique dans les aspects biopsychosociaux et comportementaux du syndrome de Gilles de la Tourette. Un mod\u00e8le interactif pour l\u2019int\u00e9gration des facteurs. In S. Jurado (Pr\u00e9sidence). Premier Congr\u00e8s national du syndrome de Tourette et des troubles associ\u00e9s. ASTTA, C\u00f3rdoba, Espagne.<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Accademia della Crusca (27 mai 2017). Consult\u00e9 \u00e0 partir de http:\/\/www.accademiadellacrusca.it\/it\/link-utili\/dizionari-sincronici<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Dizionari Corrieri (27 mai 2017). Consult\u00e9 \u00e0 partir de http:\/\/dizionari.corriere.it\/dizionario_sinonimi_contrari\/T\/ticchio.shtml<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Jankovic, J., &amp; Fahn, S. (1986). The phenomenology of tics. Movement Disorders, 1(1), 17-26. http:\/\/dx.doi.org\/10.1002\/mds.870010103<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Robertson, M. (2000). Tourette syndrome, associated conditions and the complexities of treatment. Brain, 123(3), 425-462. http:\/\/dx.doi.org\/10.1093\/brain\/123.3.425<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Robertson MM &amp; Eapen V (2013). Wither the relationship between aetiology and phenotype in Tourette In: Leckman JF, Martino, D (Eds.), Tourette Syndrome. Oxford University Press, New York, pp. 361\u2013394.<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Freeman, R.D., Zinner, S.H., Muller-Vahl, K.R., Fast, D.K., Burd, L.J., Kano, Y., Rothenberger, A., Roessner, V., Kerbeshian, J., Stern, J.S., Jankovic, J., Loughin, T., Janik, P., Shady, G., Robertson, M.M., Lang, A.E., Budman, C., Magor, A., Bruun, R., and Berlin, C.M. Jr. (2009) Coprophenomena in Tourette syndrome. Med. Child Neurol, 51: 218\u2013227. DOI:10.1111\/j.1469-8749.2008.03135.x<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Espert, R., Gadea, M., Ali\u00f1o, M. et Oltra-Cucarella, J. (2017). Neuropsychologie du trouble de Tourette : cognition, imagerie c\u00e9r\u00e9brale et cr\u00e9ativit\u00e9. Revista de Neurolog\u00eda, 64 (s01): S65-S72. http:\/\/www.neurologia.com\/articulo\/2017015<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Jeremy Willsey, Thomas V. Fernandez, Dongmei Yu, Robert A. King, Andrea Dietrich, Jinchuan Xing, Stephan J. Sanders, Jeffrey D. Mandell, Alden Y. Huang, Petra Richer, Louw Smith, Shan Dong, Kaitlin E. Samocha, (2017). De novo coding variants are strongly associated with Tourette Disorder. Neuron, 94 (3), 486\u2013499. DOI: http:\/\/dx.doi.org\/10.1016\/j.neuron.2017.04.024<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Ganos, C., Roessner, V., &amp; M\u00fcnchau, A. (2013). The functional anatomy of Gilles de la Tourette. Neuroscience &amp; Biobehavioral Reviews, 37(6), 1050-1062.<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Commission europ\u00e9enne (27 mai 2017). Les maladies rares : un d\u00e9fi pour l&rsquo;Europe. Consult\u00e9 \u00e0 partir de : http:\/\/ec.europa.eu\/health\/ph_threats\/non_com\/docs\/raredis_comm_es.pdf<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Minist\u00e8re de l&rsquo;\u00c9conomie, de l&rsquo;Industrie et de la Comp\u00e9titivit\u00e9 et Instituto de Salud Carlos III (27 mai 2017). Registre national des maladies rares. Consult\u00e9 \u00e0 partir de : https:\/\/registroraras.isciii.es\/Comun\/Inicio0.aspx<\/em><\/li>\n\n\n\n<li class=\"has-xs-font-size\"><em>Institut national de la statistique (27 mai 2017). Consult\u00e9 \u00e0 partir de : http:\/\/www.ine.es\/dyngs\/INEbase\/es\/operacion.htm?c=Estadistica_C&amp;cid=1254736176951&amp;menu=ultiDatos&amp;idp=1254735572981<\/em><\/li>\n<\/ol>\n\n\n\n<h3 class=\"wp-block-heading\">Si vous avez aim\u00e9 cet article sur le syndrome de Tourette, vous pourriez \u00eatre int\u00e9ress\u00e9 par les articles suivants de NeuronUP :<\/h3>\n\n<div class=\"mai-grid entries entries-grid has-boxed has-image-full\" style=\"--entry-title-font-size:var(--font-size-lg);--align-text:start;--entry-meta-text-align:start;\"><div class=\"entries-wrap has-columns\" style=\"--columns-xs:1\/1;--columns-sm:1\/1;--columns-md:1\/3;--columns-lg:1\/3;--flex-xs:0 0 var(--flex-basis);--flex-sm:0 0 var(--flex-basis);--flex-md:0 0 var(--flex-basis);--flex-lg:0 0 var(--flex-basis);--column-gap:var(--spacing-lg);--row-gap:var(--spacing-lg);--align-columns:start;\"><article class=\"entry entry-grid is-column has-entry-link has-image has-image-first type-post 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class=\"entry-image-link\" href=\"https:\/\/neuronup.com\/fr\/actualites-de-la-stimulation-cognitive\/neurorehabilitation-ou-neurorehabilitation-comment-secrit\/\" tabindex=\"-1\" aria-hidden=\"true\"><img decoding=\"async\" width=\"400\" height=\"300\" src=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2023\/02\/neurorrehabilitaciom-cerebro-1-1.webp\" class=\"entry-image size-landscape-sm\" alt=\"Repr\u00e9sentation 3D d\u2019un cerveau bleu avec r\u00e9seau neuronal et points rouges sur fond noir, symbolisant l\u2019activit\u00e9 c\u00e9r\u00e9brale.\" srcset=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2023\/02\/neurorrehabilitaciom-cerebro-1-1-300x225.webp 300w, https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2023\/02\/neurorrehabilitaciom-cerebro-1-1-768x576.webp 768w, https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2023\/02\/neurorrehabilitaciom-cerebro-1-1-1024x768.webp 1024w, 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am\u00e9liorer la cognition sociale chez les adultes\" itemscope itemtype=\"https:\/\/schema.org\/CreativeWork\"><a class=\"entry-image-link\" href=\"https:\/\/neuronup.com\/fr\/activites-de-neuro-reeducation\/activites-pour-les-fonctions-cognitives\/activites-de-cognition-sociale\/nouvelle-activite-numerique-reaction-emotive-face-a-des-situations-pour-ameliorer-la-cognition-sociale-chez-les-adultes\/\" tabindex=\"-1\" aria-hidden=\"true\"><img decoding=\"async\" width=\"400\" height=\"300\" src=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/11\/Reaction-emotive-face-aux-situations-1-400x300.webp\" class=\"entry-image size-landscape-sm\" alt=\"Une femme exprimant une r\u00e9action de d\u00e9go\u00fbt ou de surprise, avec deux blocs de texte \u00e9voquant des th\u00e8mes li\u00e9s aux enfants.\" srcset=\"https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/11\/Reaction-emotive-face-aux-situations-1-400x300.webp 400w, https:\/\/neuronup.com\/fr\/wp-content\/uploads\/2024\/11\/Reaction-emotive-face-aux-situations-1-800x600.webp 800w\" sizes=\"(max-width:599px) 599px, (min-width:600px) and (max-width: 799px) 799px, (min-width:800px) and (max-width: 999px) 333px, (min-width:1000px) 400px\" \/><\/a><div class=\"entry-wrap entry-wrap-grid\"><h3 class=\"entry-title\" itemprop=\"headline\"><a class=\"entry-title-link\" href=\"https:\/\/neuronup.com\/fr\/activites-de-neuro-reeducation\/activites-pour-les-fonctions-cognitives\/activites-de-cognition-sociale\/nouvelle-activite-numerique-reaction-emotive-face-a-des-situations-pour-ameliorer-la-cognition-sociale-chez-les-adultes\/\" rel=\"bookmark\">Nouvelle activit\u00e9 num\u00e9rique : R\u00e9action \u00e9motive face \u00e0 des situations pour am\u00e9liorer la cognition sociale chez les adultes<\/a><\/h3>\n<\/div><\/article><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Deconstruyendo el s\u00edndrome de Tourette<\/p>\n","protected":false},"author":177,"featured_media":27399,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_genesis_hide_title":false,"_genesis_hide_breadcrumbs":false,"_genesis_hide_singular_image":false,"_genesis_hide_footer_widgets":false,"_genesis_custom_body_class":"","_genesis_custom_post_class":"","_genesis_layout":"","footnotes":""},"categories":[604],"tags":[881],"class_list":{"2":"type-post","7":"category-maladies-rares","8":"tag-maladies-rares","9":"entry"},"acf":[],"_links":{"self":[{"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/posts\/27113","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/users\/177"}],"replies":[{"embeddable":true,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/comments?post=27113"}],"version-history":[{"count":0,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/posts\/27113\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/media\/27399"}],"wp:attachment":[{"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/media?parent=27113"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/categories?post=27113"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuronup.com\/fr\/wp-json\/wp\/v2\/tags?post=27113"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}